ULTRASOUND DIAGNOSIS OF NONCOMPACTION OF THE LEFT VENTRICULAR MYOCARDIUM
Rubrics: CASE REPORT
Authors:
1.
Irkutsk State Regional Children’s Clinical Hospital
(Ultrasonic Medical Investigation Specialist)
Irkutsk, Irkutsk region, Russian Federation
Irkutsk, Irkutsk region, Russian Federation
2.
Irkutsk State Medical Academy of Postgraduate Education
(Head of the Department of Pediatrics)
Irkutsk, Irkutsk region, Russian Federation
Irkutsk, Irkutsk region, Russian Federation
3.
Irkutsk State Medical Academy of Postgraduate Education
(Teaching Assistant at the Department of Pediatrics)
Irkutsk, Irkutsk region, Russian Federation
Irkutsk, Irkutsk region, Russian Federation
4.
Irkutsk, Irkutsk region, Russian Federation
Type:
Article
Pages:
from 186
to 192
Status:
Published
Received:
18.10.2017
Accepted:
22.11.2017
Published:
22.11.2017
Subject area:
UDK 61 Медицина. Охрана здоровья
Language:
Russian
Keywords:
ul'trazvukovaya diagnostika, kardiomiopatiya, nekompaktnyy miokard levogo zheludochka, ehokardiografiya, deti
Abstract (English):
Opisany klinicheskie sluchai redko vstrechayuschegosya, geneticheski geterogennoy kardiomiopatii – nekompaktnogo miokarda levogo zheludochka u 4 detey (3 mal'chika i 1 devochka) v vozraste ot 2 mesyacev do 6 let. Predstavleno opisanie ehokardiograficheskoy kartiny v sootvetstvii s sovremennymi diagnosticheskimi kriteriyami. Nekompaktnyy miokard levogo zheludochka vyyavlen u 3, levogo i pravogo zheludochka – u 1. Sredi 4 pacientov u 3 nekompaktnyy miokard byl samostoyatel'nym zabolevaniem, a esche u 1 on vyyavlen na fone neyrofibromatoza I tipa, v sochetanii s dilataciey koronarnyh arteriy i perikardial'nym vypotom. Troe iz 4 pacientov postupili s yavleniyami tyazheloy serdechnoy nedostatochnosti 3-4 FK po NYHA. Privedeny ehokardiogrammy s opisaniem harakternyh osobennostey zabolevaniya (gipertrabekulyarnost', gubchatyy miokarda, tipichnoe sootnoshenie nekompaktnogo i kompaktnogo sloya ot 2,0 do 2,6. Vsem 4 pacientam byli naznacheny preparaty dlya lecheniya serdechnoy nedostatochnosti (diuretiki, beta-blokatory, kapoten, v odnom sluchae digoksin); dvoe poluchali antitromboticheskuyu terapiyu (aspirin, varfarin). Privedeny rezul'taty dinamicheskogo nablyudeniya pacientov s NMLZh v techenie neskol'kih let na fone lecheniya s ocenkoy razlichiy ul'trazvukovoy kartiny. U 2 pacientov iz 4 detey na fone terapii zastoynoy serdechnoy nedostatochnosti pri nablyudenii ≥ 5 let frakciya izgnaniya levogo zheludochka vozrosla – kak po Simpson, tak i po Teicholz, odnovremenno so snizheniem stepeni serdechnoy nedostatochnosti; a esche u 2 pri nablyudenii ot 2 mes. do 5 let frakciya izgnaniya levogo zheludochka tozhe uvelichilas', no sohranyaetsya zastoynaya serdechnaya nedostatochnost' 3 FK i priznaki pravozheludochkovoy nedostatochnosti.
Opisany klinicheskie sluchai redko vstrechayuschegosya, geneticheski geterogennoy kardiomiopatii – nekompaktnogo miokarda levogo zheludochka u 4 detey (3 mal'chika i 1 devochka) v vozraste ot 2 mesyacev do 6 let. Predstavleno opisanie ehokardiograficheskoy kartiny v sootvetstvii s sovremennymi diagnosticheskimi kriteriyami. Nekompaktnyy miokard levogo zheludochka vyyavlen u 3, levogo i pravogo zheludochka – u 1. Sredi 4 pacientov u 3 nekompaktnyy miokard byl samostoyatel'nym zabolevaniem, a esche u 1 on vyyavlen na fone neyrofibromatoza I tipa, v sochetanii s dilataciey koronarnyh arteriy i perikardial'nym vypotom. Troe iz 4 pacientov postupili s yavleniyami tyazheloy serdechnoy nedostatochnosti 3-4 FK po NYHA. Privedeny ehokardiogrammy s opisaniem harakternyh osobennostey zabolevaniya (gipertrabekulyarnost', gubchatyy miokarda, tipichnoe sootnoshenie nekompaktnogo i kompaktnogo sloya ot 2,0 do 2,6. Vsem 4 pacientam byli naznacheny preparaty dlya lecheniya serdechnoy nedostatochnosti (diuretiki, beta-blokatory, kapoten, v odnom sluchae digoksin); dvoe poluchali antitromboticheskuyu terapiyu (aspirin, varfarin). Privedeny rezul'taty dinamicheskogo nablyudeniya pacientov s NMLZh v techenie neskol'kih let na fone lecheniya s ocenkoy razlichiy ul'trazvukovoy kartiny. U 2 pacientov iz 4 detey na fone terapii zastoynoy serdechnoy nedostatochnosti pri nablyudenii ≥ 5 let frakciya izgnaniya levogo zheludochka vozrosla – kak po Simpson, tak i po Teicholz, odnovremenno so snizheniem stepeni serdechnoy nedostatochnosti; a esche u 2 pri nablyudenii ot 2 mes. do 5 let frakciya izgnaniya levogo zheludochka tozhe uvelichilas', no sohranyaetsya zastoynaya serdechnaya nedostatochnost' 3 FK i priznaki pravozheludochkovoy nedostatochnosti.
Keywords:
ul'trazvukovaya diagnostika, kardiomiopatiya, nekompaktnyy miokard levogo zheludochka, ehokardiografiya, deti
ul'trazvukovaya diagnostika, kardiomiopatiya, nekompaktnyy miokard levogo zheludochka, ehokardiografiya, deti
1. Spislit ehokardiografiya
