student
Tula, Russian Federation
UDC 61
Granulomatosis with polyangiitis is a systemic autoimmune disease characterized by damage to small and medium-sized vessels, the formation of granulomas, and the formation of antibodies to neutrophil cytoplasm (ANCA). The prevalence of the disease is steadily increasing, affecting the working-age population. Late diagnosis and delayed treatment lead to rapid progression of the disease and death. The article presents a case of granulomatosis with polyangiitis with damage to the kidneys, upper respiratory tract, skin, and vessels, ANCA-positive in a 49-year-old man. The diagnosis was made in a timely manner by a general practitioner, which allowed for the initiation of pathogenetically based treatment with glucocorticosteroids and cyclophosphamide, with positive results.
granulomatosis with polyangiitis, ANCA, hemorrhagic rash, arthritis, and nephritis.
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