Moskva, Netherlands
The paper presents a clinical case of abnormality of the structure of the aortic valve. Congenital defects of the valve structures are widespread among the population of Russia. A four-cusped aortic valve is a rare defeat of the valve structure, which occurs during embryogenesis. Most cases are encountered incidentally during aortic valve surgery or autopsy. This state frequently progresses to aortic regurgitation, which can manifest in adulthood and requires surgical treatment. Sometimes, this abnormality can be associated with other malformations, the most common - with coronary artery abnormality. There are no gender differences in the detection of this disease. It should be noted that the identification of this disease can be in various age groups. It was found that in 25% of patients for a long time, this abnormality is asymptomatic. Clinical manifestations begin to appear in middle age and in 70 years a distinct clinical picture seen in almost 75% of patients with an abnormality of the valve. This article describes a clinical case in young man. The authors present the possibilities of diagnosis and strategy of treatment.
heart defect, aortic valve, four-cusped aortic valve.
1. Gans Bankl. Vrozhdennye poroki serdtsa i krupnykh sosudov. Moscow: Meditsina; 1980. Russian.
2. Ivanov DV. Ishemicheskaya bolezn´ serdtsa i kletochnye tekhnologii. Vestnik novykh meditsinskikh tekhnologiy. 2009;16(2):177. Russian.
3. Ivanov DV. Kachestvo zhizni pri kardiomiopatiyakh posle vozdeystviya stvolovykh kletok. Vestnik novykh meditsinskikh tekhnologiy. 2009;16(2):177. Russian.
4. Kosach GA, Evzhanov A, Serbin VI, et al. Chetyrekhstvorchatyy aortal´nyy klapan. Kardiologiya. 1982;22(4):113-4. Russian.
5. Kharvi Fegenbaum. Ekhokardiografiya. Moscow: «Samizdat»; 2004. Russian.
6. Feldman BJ, Khandheria BK, Warnes CA, et al. Incidence, description and functional assessment ofisolated quadricuspid aortic valves. Am. J.Cardiol. 1990;65(13):937-8.
7. Hayakawa M, Asai T, Kinoshita T, Suzuki T. Quadricuspid Aortic Valve: A Report on a 10-Year Case Series and Literature Review. Ann Thorac Cardiovasc Surg; 2014.
8. Hurwitz LE, Roberts WC. Quadricuspid semilunar valve. Am. J. Cardiol. 1973;31:623-6.
9. Janssens U, Klues HG, Hanrath P. Congenital quadricuspid aortic valve anomaly associated with hypertrophic nonobstructive cardiomyopathy: a case report and review of the literature. Heart.1997;78(1):83-7.
10. Kanno M, Satoh M, Kurihara S, et al. Quadricuspid aortic valve: three case reports and review of the literature. Kyobu. Geka. 1994;47(5):387-90.
11. Kucukoglu MS, Erdogan I, Okcun B, et al. Quadricuspid aortic valve abnormality associated with aortic stenosis and aortic insufficiency. J. Am. Soc. Echocardiogr. 2002;15(1):90-2.
12. Simonds JP. Congenital malformations of the aortic and pulmonary valves. Am. J. Med. Sci. 1923; 166:584-95.
